Oral Surg Oral Med Oral Pathol. Dec;68(6) Familial gigantiform cementoma: classification and presentation of a large pedigree. Young SK(1). Gigantiform cementoma is a rare, benign fibro-cemento-osseous disease of the jaws, seen most frequently in young girls. Radiographically, it typically presents. PDF | Familial gigantiform cementoma is an exceedingly rare but distinct subtype of cemento-osseous-fibrous lesion. Undocumented.

Author: Akisida Voodoolkree
Country: Romania
Language: English (Spanish)
Genre: Automotive
Published (Last): 15 June 2018
Pages: 10
PDF File Size: 1.53 Mb
ePub File Size: 10.80 Mb
ISBN: 177-8-65606-464-5
Downloads: 19923
Price: Free* [*Free Regsitration Required]
Uploader: Mikagal

Focal OD is a solitary lesion affecting a single area in the jaw bone and mainly the posterior quadrant of the jaws.

Gigantiform cementoma – Wikipedia

Circumstantial evidence and thorough reasoning were presented in his article for differential diagnosis with other easily mistaken diseases, such as Paget disease, cemento-ossifying fibromas and osteogenesis imperfecta. J Neurosurg Pediatr ; 7: According to the World Health Organization classification of osseous dysplasias ODFGC is generally regarded as an odontogenic lesion that shares a same periodontal ligament origin with focal, periapical.

EllisDerek Gifantiform. Abstract The objective of this report is to present an unusual case of a gigantiform cementoma manifesting with gross expansion of the maxilla in a 6-year-old black female. From Wikipedia, the free encyclopedia.

Despite the paucity of information regarding FGC, DEA, as we believe, carries diagnostic and therapeutic implications, along with other radiographic examinations.

Familial gigantiform cementoma: classification and presentation of a large pedigree.

The maxillary sinus and nasal passage are obliterated and the midline is slightly deviated to the right. The feasibility of using fibular flaps was ruled out in view of his unfortunate history of frequent lower-extremity fractures.

Published online Mar 7. Periprosthetic bone mineral density changes after unicondylar knee arthroplasty. J Dent Assoc S Afr ; Noura AlsufyaniErnest W.

Views Read Edit View history. Benign cementoblastoma is a benign odontogenic neoplasm of cementoblastic origin, occurs cemntoma commonly in the mandibular first molar area, is attached to the root of an associated tooth and is cementoam by a well-defined radiolucent margin. S50—S70 [ PubMed ]. Loss of lamina dura, decreased skull bone density, and sporadic bony defects all served as convincing evidence of the serious gigantidorm fragility. B Preoperative panorex X-ray showed a characteristic radiographic feature of familial gigantiform cementoma FGC with well-circumscribed radiopaque areas involving all quadrants of the jaw, with mandible being more severely damaged.


Retrieved from ” https: Surgery with recontouring and shaving intent was initially attempted in a local institution about 7 months ago, but in vain. Expert curators review the literature and organize it to facilitate your work.

Before referral, he had experienced 4 times of fractures in bilateral lower extremities within 4 years. Familial gigantiform cementoma is an exceedingly rare but distinct subtype of cemento-osseous-fibrous lesion. Since then, supplementation of calcium and vitamin D had been prescribed as a method to ameliorate the general calcium metabolism disorder. Arteriovenous malformation of the scalp with cerebral steal. The swelling depressed the lower eyelid with exposure of the sclera, and expanded the palate.

In addition, FGC also carries a striking tendency toward more exuberant growth with multiquadrant jaw involvement. During the rapid growth phase gigantiformm FGC in mandible and maxilla, the other bones, especially long bones in lower extremities, were simultaneously undergoing a calcium absorption or transportation problem, as was reflected gigantiiform the gigantifform radiographic changes in our adolescent patient. Please consider making a donation now and again in the future.

For sake of differential diagnosis with hyperparathyroidism-jaw tumor HPT-JT syndrome, 4 several laboratory analyses, which included serum parathyroid hormone PTHphosphate levels, calcium levels, and alkaline phosphatase Cementmoa activity, were undertaken accordingly.

While the OMIM database is open to the public, users seeking information about a personal medical or genetic condition are urged to consult with a qualified physician for diagnosis and for answers to personal questions.

A diagnosis of a gigantiform cementoma was made.

Head and Neck Tumours. Familial occurrence of periapical cemental dysplasia. A provisional diagnosis of an osteoma was made and the lesion was enucleated through the buccal cortical plate. It affects mostly Caucasian people under the age of C Lateral view of FGC. The lesions had an early age of onset and developed slowly.


Periapical OD occurs in the anterior mandible and involves the periapical regions of a few incisor teeth, while florid OD is more extensive and can involve the mandible bilaterally gigamtiform all four jaw quadrants.

Familial Gigantiform Cementoma

Microscopic examination showed mineralized bone with obliterated marrow spaces containing inactive fibrous tissue Figure 5. The radiological differential diagnosis of a well-defined, expansive mineralized mass in the jawbone includes benign cementoblastoma, osteoma, ossifying fibroma and FGC. Gigantiform cementoma in a child. D Postoperative view of patient after bilateral mandibulectomy.

Gigantiform cementoma in a child

Large vascular malformation in a child presenting with vascular steal phenomenon managed with pial synangiosis. Macdonald Oral surgery, oral medicine, oral pathology and….

Please help improve this article by adding citations to reliable sources. Therefore, we agree with Noffke et al 14 and Finical 15 in resorting to a complete resection of FGC cemenyoma curative purposes whenever feasible.

Admittedly, not every FGC case will present such evident array of disorganized conditions. According to Young et al. The growth of the disfigured mandible had not givantiform been deterred, but instead, accelerated, accompanied by teeth loss and altered dietary patterns.

Citations Publications citing this paper. It is benign, but without intervention it can result in severe disfigurement of the jaw. E Postoperative panorex X-ray showed vascularized iliac bone flap for reconstruction.

Abstract Familial gigantiform cementoma is an exceedingly rare but distinct subtype of cemento-osseous-fibrous lesion.